Results for
""Phenylbutyrates""[mesh_terms]

Tauro-Urso-Deoxycholic Acid Trials in Amyotrophic Lateral Sclerosis: What is Achieved and What to Expect.

Antoniangela Cocco, Maria Lo Giudice, Giorgio Reggiardo, Stefania Lalli, Alberto Albanese

Clinical drug investigation 2023;43(12):893-903

Role of glutamine depletion in severe illness.

D Darmaun

Diabetes, nutrition & metabolism 2000;13(1):25-30

Sodium Phenylbutyrate and Tauroursodeoxycholic Acid: A Story of Hope Turned to Disappointment in Amyotrophic Lateral Sclerosis Treatment.

Arsh Ketabforoush, Bahram Haghi Ashtiani, Mohamad Amin Habibi, Armin Ariaei, Mohammad Taghi Joghataei, W David Arnold, Maryam Khalili, Fereshteh Azedi, Faezeh Faghihi

Clinical drug investigation 2024;44(7):495-512

Comparison Between Dichloroacetate and Phenylbutyrate Treatment for Pyruvate Dehydrogenase Deficiency.

Sook Hui Tay, Teck Yew Low, Simon P Dawson, Timothy Simpson, Patricia Karissa, Fatimah Diana Amin Nordin, Yuh-Fen Pung, Pey Yee Lee, Shamsul Mohd Zain

British journal of biomedical science 2022;79():10382

Analysis of sodium phenylbutyrate and taurursodiol survival effect in ALS using external controls.

Sabrina Paganoni, Melanie Quintana, Alexander V Sherman, Matteo Vestrucci, Yuehui Wu, Jamie Timmons, Merit Cudkowicz

Annals of clinical and translational neurology 2023;10(12):2297-2304

Pharmacological treatment of the ion transport defect in cystic fibrosis.

G M Roomans

Expert opinion on investigational drugs 2001;10(1):1-19

Novel Ammonia-Lowering Agents for Hepatic Encephalopathy.

Don C Rockey, Robert S Rahimi

Clinics in liver disease 2016;19(3):539-49

Phase II trial of sodium phenylbutyrate and taurursodiol in Wolfram syndrome.

Fumihiko Urano, Bess A Marshall, Stacy Hurst, Amy Robichaux-Viehoever, Saumel Ahmadi, Tamara Hershey, Gregory Van Stavern, Paulina Cruz Bravo, Jennifer Powers Carson, John Pesko, Kelly Fox, Nathalie Erpelding, Camille L Bedrosian

The Journal of clinical investigation 2026;136(10):

A randomized trial to study the comparative efficacy of phenylbutyrate and benzoate on nitrogen excretion and ureagenesis in healthy volunteers.

Mahshid Azamian, Juan C Marini, Mahmoud A Mohammad, Inka C Didelija, Ann McMeans, Allison Tam, Umang Agarwal, Sandesh C S Nagamani

Genetics in medicine : official journal of the American College of Medical Genetics 2018;20(7):708-716

Ammonia control in children with urea cycle disorders (UCDs); phase 2 comparison of sodium phenylbutyrate and glycerol phenylbutyrate.

Uta Lichter-Konecki, G A Diaz, J L Merritt, A Feigenbaum, C Jomphe, J F Marier, M Beliveau, J Mauney, K Dickinson, A Martinez, M Mokhtarani, B Scharschmidt, W Rhead

Molecular genetics and metabolism 2012;103(4):323-9

Treatment of hyperammonemia in liver failure.

Maria Jover-Cobos, Varun Khetan, Rajiv Jalan

Current opinion in clinical nutrition and metabolic care 2014;17(1):105-10

Evidence of CFTR function in cystic fibrosis after systemic administration of 4-phenylbutyrate.

Pamela L Zeitlin, Marie Diener-West, Lois Brass-Ernst, Carlton K K Lee, Michael P Boyle, Ronald C Rubenstein

Molecular therapy : the journal of the American Society of Gene Therapy 2003;6(1):119-26

Glycerol phenylbutyrate treatment in children with urea cycle disorders: pooled analysis of short and long-term ammonia control and outcomes.

Susan A Berry, Uta Lichter-Konecki, George A Diaz, Shawn E McCandless, William Rhead, Wendy Smith, Cynthia Lemons, Sandesh C S Nagamani, Dion F Coakley, Masoud Mokhtarani, Bruce F Scharschmidt, Brendan Lee

Molecular genetics and metabolism 2014;112(1):17-24

Direct acting inhibitors of ammoniagenesis: a role in post-TIPS encephalopathy?

Stephen H Caldwell, Winston A Ally, Nitin K Ahuja

Annals of hepatology 2014;13(2):179-86