Updates in Nutrition Management of Cystic Fibrosis in the Highly Effective Modulator Era.

Alexandra Wilson, Kimberly Altman, Terri Schindler, Sarah Jane Schwarzenberg

Journal: Clinics in chest medicine 2022;43(4):727-742

PMID: 36344077

Full Text on Elsevier Science View on PubMed

Abstract

Attainment and maintenance of good nutrition has been an important aspect of management in cystic fibrosis (CF) for decades. In the era of highly effective modulator therapy for CF, the quality of the nutrients we recommend is increasingly important. Our therapy must support our patients' health for many years beyond what we previously thought. Preventing cardiovascular disease, reducing hyperlipidemia, and optimizing lean body mass for active, longer lives now join the long-standing goal of promoting lung function through nutrition. This chapter summarizes recent developments in nutrition in people with CF, with an eye to the evolution of our practice.

Address: Cystic Fibrosis Clinical Research, Clinical Research Services, National Jewish Health, 1400 Jackson Street, K333, Denver, CO 80206, USA.; Gunnar Esiason Adult Cystic Fibrosis and Lung Center, Columbia University Medical Center, New York Presbyterian Hospital, New York, NY, USA.; Pediatric Pulmonology, University Hospitals Cleveland Medical Center, Rainbow Babies and Children's Hospital.; Department of Pediatrics; University of Minnesota Masonic Children's Hospital, Academic Office Building, 2450 Riverside Avenue South AO-201, Minneapolis, MN 55454, USA. Electronic address: [email protected].

DOI: 10.1016/j.ccm.2022.06.012

Link outs

Free resources

Medical:

Subscription / membership required

Full Text Sources:

MeSH Terms: Humans, Cystic Fibrosis, Cystic Fibrosis Transmembrane Conductance Regulator, Mutation