Aortopathy in Congenital Heart Disease.

Timothy B Cotts, Katherine B Salciccioli, Sara K Swanson, Anji T Yetman

Journal: Cardiology clinics 2021;38(3):325-336

PMID: 32622488

Full Text on Elsevier Science View on PubMed

Abstract

Aortic dilatation is common in patients with congenital heart disease and is seen in patients with bicuspid aortic valve and those with conotruncal congenital heart defects. It is important to identify patients with bicuspid aortic valve at high risk for aortic dissection. High-risk patients include those with the aortic root phenotype and those with syndromic or familial aortopathies including Marfan syndrome, Loeys-Dietz syndrome, and Turner syndrome. Aortic dilatation is common in patients with conotruncal congenital heart defects and rarely results in aortic dissection.

Address: Internal Medicine and Pediatrics, University of Michigan, Michigan Congenital Heart Center, 1540 East Hospital Drive, Ann Arbor, MI 48109-4204, USA. Electronic address: [email protected].; University of Michigan, Michigan Congenital Heart Center, 1540 East Hospital Drive, Ann Arbor, MI 48109-4204, USA.; Pediatrics, University of Nebraska Medical Center, Children's Hospital & Medical Center, and Nebraska Medicine, 8200 Dodge Street, Omaha, NE 68114, USA.; Pediatrics, Aortopathy Program, University of Nebraska Medical Center, Children's Hospital & Medical Center, and Nebraska Medicine, 8200 Dodge Street, Omaha, NE 68114, USA; Medicine, Aortopathy Program, University of Nebraska Medical Center, Children's Hospital & Medical Center, and Nebraska Medicine, 8200 Dodge Street, Omaha, NE 68114, USA.

DOI: 10.1016/j.ccl.2020.04.002

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MeSH Terms: Aortic Dissection, Aorta, Aortic Diseases, Bicuspid Aortic Valve Disease, Dilatation, Pathologic, Heart Defects, Congenital, Humans, Risk Assessment