Pediatric pulmonary lymphatic flow Disorders: Diagnosis and management.

David M Biko, Yoav Dori, Melanie Savoca, Ganesh Krishnamurthy, Christopher L Smith, Pablo Laje, Jonathan J Rome, Fernando Escobar

Journal: Paediatric respiratory reviews 2021;36():2-7

PMID: 31884062

Full Text on Elsevier Science View on PubMed

Abstract

Pulmonary lymphatic flow disorders involve the abnormal lymphatic flow via lymphatic channels to the lungs and pleural space. Plastic bronchitis and chylothorax are the main complications of this abnormal lymphatic perfusion, which has been termed pulmonary lymphatic perfusion syndrome (PLPS). Following lymphatic access, dynamic contrast MR lymphangiography is the imaging modality of choice to diagnose these disorders. Management includes medical therapy, percutaneous interventions under fluoroscopy, and surgical interventions.

Address: Department of Radiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA, United States. Electronic address: [email protected].; Division of Cardiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA, United States. Electronic address: [email protected].; Division of Cardiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA, United States. Electronic address: [email protected].; Department of Radiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA, United States. Electronic address: [email protected].; Division of Cardiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA, United States. Electronic address: [email protected].; Department of Surgery, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA, United States. Electronic address: [email protected].; Division of Cardiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA, United States. Electronic address: [email protected].; Department of Radiology, Children's Hospital of Philadelphia, University of Pennsylvania Perelman School of Medicine, Philadelphia, PA, United States. Electronic address: [email protected].

DOI: 10.1016/j.prrv.2019.11.002

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MeSH Terms: Adolescent, Bronchitis, Child, Child, Preschool, Chylothorax, Contrast Media, Diet Therapy, Dietary Supplements, Disease Management, Embolization, Therapeutic, Humans, Infant, Lung Diseases, Lymphatic Abnormalities, Lymphatic Diseases, Lymphatic Vessels, Lymphography, Magnetic Resonance Imaging, Microsurgery