Nutrition: Prevention and management of nutritional failure in Cystic Fibrosis.

Jillian S Sullivan, Maria R Mascarenhas

Journal: Journal of cystic fibrosis : official journal of the European Cystic Fibrosis Society 2018;16 Suppl 2():S87-S93

PMID: 28986026

Free Full Text on Elsevier Science View on PubMed

Abstract

Close monitoring of nutritional status is critical to the overall health of a patient with CF. As part of routine CF care, measurement of weight and height (and calculation of weight/length or BMI as appropriate) should be performed and analyzed at each visit. Early recognition of nutritional risk is imperative and evaluation with a multidisciplinary team should be performed to assess for caloric intake, caloric malabsorption, and other causes of poor weight gain and growth. Many tools are available to use for intervention, including oral supplementation, behavioral interventions, medications, nutritional therapies, and enteral tube feeding.

Address: Department of Pediatrics, University of Vermont Children's Hospital, Burlington, VT, USA. Electronic address: [email protected].; Department of Pediatrics, Children's Hospital of Philadelphia, Philadelphia, PA, USA. Electronic address: [email protected].

DOI: 10.1016/j.jcf.2017.07.010