Lung clearance index response in patients with CF with class III CFTR mutations.
Mica Kane, Tanja Gonska, Renee Jensen, Julie Avolio, Michelle Klingel, Sanja Stanojevic, Felix Ratjen
Journal: Thorax
2016;71(5):476-7
PMID: 26944510
Address:
Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada.; Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada Division of Gastroenterology and Nutrition, Department of Pediatrics, Toronto, Ontario, Canada Department of Pediatrics, University of Toronto, Ontario, Canada.; Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada Division of Gastroenterology and Nutrition, Department of Pediatrics, Toronto, Ontario, Canada.; Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada Institute of Health Policy, Management and Evaluation, University of Toronto, Ontario, Canada.; Division of Respiratory Medicine, Department of Pediatrics, Toronto, Ontario, Canada Physiology & Experimental Medicine, The Research Institute, The Hospital for Sick Children, Toronto, Ontario, Canada Department of Pediatrics, University of Toronto, Ontario, Canada.
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MeSH Terms:
Adult,
Alleles,
Aminophenols,
Cystic Fibrosis,
Cystic Fibrosis Transmembrane Conductance Regulator,
Forced Expiratory Volume,
Humans,
Maximal Midexpiratory Flow Rate,
Mutation,
Quinolones,
Saline Solution, Hypertonic,
Severity of Illness Index,
Spirometry,
Treatment Outcome