PEComa of the uterus with coexistence of situs inversus totalis, a case report and literature review.

Yang Han, Ting-ting Liu, Xue-shan Qiu, Qing-chang Li, Yi Zhao, Xiao-Yan Pang, En-hua Wang

Journal: Diagnostic pathology 2016;10():142

PMID: 26268324

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Abstract

PEComas are a group of very rare mesenchymal neoplasms, which express myogenic and melanocytic markers, such as HMB-45 and actin. Situs inversus totalis represents a complete left to right side transposition of the asymmetrical thoracic and abdominal organs and incorporates dextrocardia. The presence of uterus PEComa in the setting of situs inversus totalis is extremely rare. Here, we report a case of PEComa of uterus with coexistence of situs inversus totalis and review the literatures. To the best of our knowledge this is the fist report of a uterus PEComa patient with situs inversus totalis.

Address: Department of Pathology, The First Affiliated Hospital of China Medical University, Shenyang, China. [email protected].; Department of General Surgery, The First Affiliated Hospital of China Medical University, Shenyang, China. [email protected].; Department of Pathology, The First Affiliated Hospital of China Medical University, Shenyang, China. [email protected].; Department of Pathology, The First Affiliated Hospital of China Medical University, Shenyang, China. [email protected].; Department of Obstetrics and Gynecology, The First Affiliated Hospital of China Medical University, Shenyang, China. [email protected].; Department of Obstetrics and Gynecology, The First Affiliated Hospital of China Medical University, Shenyang, China. [email protected].; Department of Pathology, The First Affiliated Hospital of China Medical University, Shenyang, China. [email protected].

DOI: 10.1186/s13000-015-0351-8

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https://scite.ai/reports/26268324

MeSH Terms: Adult, Biomarkers, Tumor, Female, Humans, Immunohistochemistry, Perivascular Epithelioid Cell Neoplasms, Situs Inversus, Uterine Neoplasms